A Rare Long Term Survival Case of Complete Pentalogy of Cantrell in Adult after One-Staged Surgery  

作　　者：Hao Hong Nianguo Dong Mingxing Xie Lin Li Si Chen Wengang Sun Xiaoqing Hu 

机构地区：[1]Department of Cardiovarscular Surgery,Union Hospital,Tongji Medical College,Huazhong University of Science and Technology,Wuhan,430022,China [2]Department of Ultrasound,Union Hospital,Tongji Medical College,Huazhong University of Science and Technology,Wuhan,430022,China [3]Department of Radiology,Union Hospital,Tongji Medical College,Huazhong University of Science and Technology,Wuhan,430022,China

出　　处：《Congenital Heart Disease》2021年第5期513-518,共6页先天性心脏病（英文）

基　　金：Supported by grants from the National Natural Science Foundation of China(81873502 and 31330029);the Fundamental Research Funds for the Central Universities(2017KFYXJJ250);Scientific Research Fund of Union Hospital,Tongji Medical College,Huazhong University of Science and Technology(02.03.2017-307).

摘　　要：Pentalogy of Cantrell is a rare congenital abnormality.Even with high-quality medical care and staged corrective surgeries in professional hospitals,the mortality rate is still very high and long-term prognosis is poor.Survival is largely determined by the complexity and severity of cardiac abnormalities,the efficiency of abdominal wall closure and postoperative complications.A 24-year-old male patient with complete pentalogy of Cantrell was diagnosed.One-stage surgical repair of all abnormalities were completed.The patient recovered well and had been follow-up for 7 years.He has a good cosmetic outcome,with no signs of cardiac dysfunction.No complications were noted.

关 键 词：Pentalogy of cantrell ADULT one-stage surgery 

分 类 号：R73[医药卫生—肿瘤]