Chiari畸形Ⅰ型合并脊髓空洞症的诊断与治疗进展  

Progress in Diagnosis and Treatment of Chiari Malformation TypeⅠwith Syringomyelia

作　　者：黄南勇 刘俊[1] 姚浩群[1] HUANG Nan-yong;LIU Jun;YAO Hao-qun(Department of Orthopedics,the First Affiliated Hospital of Nanchang University,Nanchang 330006,China)

机构地区：[1]南昌大学第一附属医院骨科,南昌330006

出　　处：《实用临床医学（江西）》2023年第4期125-130,共6页Practical Clinical Medicine

摘　　要：Chiari畸形(Chiari malformation,CM)也称小脑扁桃体下疝畸形,是一种罕见的颅脑交界性疾病,以CMⅠ型最常见,其特征是小脑扁桃体向下疝入椎管内的颅颈交界区,常合并脊髓空洞症(syringomyelia,SM)。目前临床对CMⅠ型合并SM的诊断和治疗仍未达成共识。文章就近年来CM及SM的发病机制、CMⅠ型合并SM诊断及治疗研究进展进行综述,旨在为临床寻找CMⅠ型合并SM的最佳诊疗方案提供参考。Chiari malformation(CM)also known as cerebellar tonsillar hernia malformation,is a craniocervical junction disease,and CM typeⅠis the most common,mainly manifested by the herniation of cerebellar tonsils into the spinal canal and often complicated by syringomyelia(SM).At present,there is no consensus on the diagnosis and treatment of CM typeⅠwith SM.This paper reviews the recent progress in the pathogenesis of CM and SM,the diagnosis and treatment of CM typeⅠwith SM,aiming to provide reference for the optimal diagnosis and treatment of CM typeⅠwith SM.

关 键 词：Chiari畸形 Ⅰ型 小脑扁桃体下疝 脊髓空洞症 发病机制 诊断 治疗 

分 类 号：R742[医药卫生—神经病学与精神病学]