肺上皮样血管内皮瘤影像表现及临床特点  

Imaging manifestations and clinical features of pulmonary epithelioid hemangioendothelioma

作　　者：姜楠[1] 胡春洪[1] 胡粟[1] 平小夏[1] 孟倩[1] 陈蒙[1] 覃玲艳 陈澄[3] JIANG Nan;HU Chunhong;HU Su;PING Xiaoxia;MENG Qian;CHEN Meng;QIN Lingyan;CHEN Cheng(Department of Radiology,Suzhou,Jiangsu Province 215006,China;Department of Pathology,Suzhou,Jiangsu Province 215006,China;Department of Respiratory and Critical Care Medicine,the First Affiliated Hospital of Soochow University,Suzhou,Jiangsu Province 215006,China)

机构地区：[1]苏州大学附属第一医院放射科,江苏苏州215006 [2]苏州大学附属第一医院病理科,江苏苏州215006 [3]苏州大学附属第一医院呼吸与危重症医学科,江苏苏州215006

出　　处：《实用放射学杂志》2023年第8期1241-1243,共3页Journal of Practical Radiology

摘　　要：目的探讨肺上皮样血管内皮瘤(P-EHE)的影像表现及临床、病理特点。方法回顾性分析经病理证实的9例P-EHE患者的临床病理资料及影像表现,总结分析其特点。结果9例患者病灶发生于两肺9例,位于肝脏4例,肋骨3例,胸膜2例,髋关节1例,肘关节1例,颈椎1例,腹膜后1例。胸部CT表现为两肺多发小结节7例,肺内肿块4例,胸膜增厚2例,胸腔积液2例。正电子发射断层显像/计算机体层成像(PET/CT)示结节或肿块葡萄糖代谢增高或轻度增高。结论P-EHE患者CT表现具有一定特征,多发结节常<2cm,多位于肺门或胸膜下血管束周围,肝脏、骨骼或胸膜等部位相继发现病变,最终确诊有赖于病理以及免疫组化检查。Objective To investigate the imaging manifestations,clinical and pathological features of pulmonary epithelioid hemangioendothelioma(P-EHE).Methods The clinicopathologic data and imaging features of 9 patients with P-EHE confirmed by pathology were analyzed retrospectively,and their characteristics were summarized and analyzed.Results Of the 9 patients,9 occurred in both lungs,4 in the liver,3 in the ribs,2 in the pleura,1 in the hip joint,l in the elbow joint,1 in the cervical spine,and 1 in the retroperitoneal space.Chest CT showed multiple small nodules in both lungs in 7 cases,pulmonary masses in 4 cases,pleural thickening in 2 cases,and pleural effusion in 2 cases.Positron emission tomography/computed tomography(PET/CT)showed increased or mildly increased glucose metabolism in the nodules or masses.Conclusion CT manifestations of P-EHE patients have certain characteristics.Multiple nodules often less than 2 cm should be located around the hilum or subpleural vascular bundles mostly,and could be found in the liver,bone,or pleura successively.The final diagnosis relies on pathology and immunohistochemistry examination.

关 键 词：上皮样血管内皮瘤 肺 计算机体层成像 

分 类 号：R734.2[医药卫生—肿瘤] R814.42[医药卫生—临床医学]