成人左肺动脉吊带合并先天性气管狭窄1例  

A case of left pulmonary artery sling combined with congenital tracheal stenosis in an adult

作　　者：盖延玲 黄海东 张伟 李翔 张晓琴 焦洋 王琴 董宇超 白冲 Gai Yanling;Huang Haidong;Zhang Wei;Li Xiang;Zhang Xiaoqin;Jiao Yang;Wang Qin;Dong Yuchao;Bai Chong(Department of Respiratory and Critical Care,First Affiliated Hospital of Naval Military Medical University,Shanghai 2004332,China)

机构地区：[1]海军军医大学附属第一医院呼吸与危重症学科,上海200433 [2]齐齐哈尔医学院附属第三医院呼吸与危重症学科 [3]中部战区总医院呼吸与危重症学科 [4]贵州中医药大学第一附属医院呼吸内科

出　　处：《中华结核和呼吸杂志》2023年第10期1011-1014,共4页Chinese Journal of Tuberculosis and Respiratory Diseases

基　　金：海军军医大学“三航”人才培养计划“领航”项目。

摘　　要：成人肺动脉吊带是一种罕见的先天性血管畸形,常伴有气管及支气管狭窄。因其具有较高的死亡风险和相对较差的预后,成人患病者鲜有报道。本文报道1例中年患者,表现为自幼活动后气促,曾于外院诊断为“气管狭窄”给予对症治疗。入院后通过多层螺旋CT(MSCT)、SYNAPES 3D影像后处理系统和支气管镜检查等明确诊断为“左肺动脉吊带合并先天气管狭窄”。本文结合相关文献回顾对该病的进行总结分析,旨在提高临床医生对该病诊治的认识。Pulmonary artery sling in adults is a rare congenital vascular malformation usually accompanied by tracheal and bronchial stenosis.Due to its high mortality risk and relatively poor prognosis,it has rarely been reported in adults.We reported a middle-aged patient who presented with shortness of breath,predominantly after activity,since childhood.He was diagnosed with"tracheal stenosis"in another hospital and received symptomatic treatment.The diagnosis of left pulmonary artery sling with congenital tracheal stenosis was confirmed by multi-slice spiral CT(MSCT),airway examination with flexible bronchoscope and 3D image post-processing system.Data from this case and the related literatures have been summarized and analyzed.This will help clinicians to improve their level of diagnosis and treatment.

关 键 词：先天性血管畸形 支气管镜检查 气管狭窄 患病者 死亡风险 临床医生 肺动脉吊带 中年患者 

分 类 号：R56[医药卫生—呼吸系统]