非手术治疗自行缓解的小脑扁桃体下疝畸形Ⅰ型伴脊髓空洞症1例报道及文献复习  

Self⁃remission of Arnold⁃Chiari malformation I with syringomyelia without surgical treatment:A case report and literature review

作　　者：饶桂兰 彭永 甘棋心 何顺清 唐艳丹 RAO Guilan;PENG Yong;GAN Qixin;HE Shunqing;DANG Yandan(Hunan University of Chinese Medicine,Changsha,Hunan 410208,China;.First Hospital Affiliated to Hunan Traditional Chinese Medical College,Zhuzhou,Hunan 412000,China)

机构地区：[1]湖南中医药大学,湖南长沙410208 [2]湖南中医药高等专科学校附属第一医院,湖南株洲412000

出　　处：《国际神经病学神经外科学杂志》2023年第4期50-53,共4页Journal of International Neurology and Neurosurgery

基　　金：湖南省中医药管理局重点课题(201915);湖南省自然科学基金(2018JJ6043);湖南省卫计委课题(B20180815);湖南中医药高等专科学校附属第一医院优秀科研创新团队(B2021-003);株洲市科技计划项目(2021-009)。

摘　　要：小脑扁桃体下疝畸形伴脊髓空洞症自发缓解或消失在成年人中极为罕见。该文报道了1例有手术治疗适应证,但未行手术治疗,而临床症状和影像学表现自发好转的病例。通过文献检索,发现了5例未经手术治疗但临床症状有不同程度好转的病例。经分析这些患者的共性,总结出了对于围绝经期女性患者,可以保守治疗,但需要定期随访,若病情恶化再行评估是否需要手术治疗。It is extremely rare for self-remission or disappearance of Arnold-Chiari malformation I with syringomyelia in adults.This article reports a case whose clinical symptoms and imaging findings improved spontaneously without surgical treatment even if the patient had indications for surgical treatment.A literature search found five patients whose clinical symptoms improved to varying degrees without receiving any surgical treatment.An analysis of the patients shows the common features as follows:for perimenopausal female patients,conservative treatment can be acceptable,but regular follow-ups are necessary;the need for surgical treatment will be assessed only when the condition worsens.

关 键 词：小脑扁桃体下疝畸形Ⅰ型 脊髓空洞症 自发好转 保守治疗 

分 类 号：R741[医药卫生—神经病学与精神病学]