阔韧带血管周上皮样细胞肿瘤一例并文献复习  

Perivascular Epithelioid Cell Tumor of Broad Ligament:A Case Report and Literature Review

作　　者：俞萍源 万桃 胡丹 姚志强 杨永秀[2] YU Pingyuan;WAN Tao;HU Dan;YAO Zhi-qiang;YANG Yong-xiu(The First Clinical Medical College of Lanzhou University,Lanzhou 730000,China;The First Hospital of Lanzhou University,Lanzhou 730000,China)

机构地区：[1]兰州大学第一临床医学院,730000 [2]兰州大学第一医院

出　　处：《国际生殖健康／计划生育杂志》2023年第6期457-461,共5页Journal of International Reproductive Health/Family Planning

摘　　要：血管周上皮样细胞肿瘤(perivascular epithelioid cell tumor,PEComa)是一种较为罕见的间叶组织来源的肿瘤,多见于育龄期女性,主要发生于肾脏、肝脏和胃肠道等部位,发生于阔韧带的病例罕见,临床上易与阔韧带肌瘤等混淆,需依靠病理形态学及免疫组织化学检查明确诊断。报告1例因下腹痛1周收住入院的患者,影像学检查示右侧盆腔肿物。腹腔镜探查术中见右侧阔韧带一大小约9 cm×8 cm的实性占位,术中病理回报梭形细胞肿瘤,瘤细胞较丰富。行腹腔镜下肿物切除术+子宫切除术+双侧输卵管切除术,经术后病理学检查确诊为阔韧带PEComa,术后随访10个月未见复发。Perivascular epithelioid cell tumor(PEComa),a rare mesenchymal tissue-derived tumor,occurs mainly in women of child-bearing age.PEComa mainly occurs in the kidney,liver,gastrointestinal tract,etc.Rare cases occur in broad ligament,which is easily confused with broad ligament myoma in clinical practice.Definitive diagnosis depends on histopathological morphology and immunohistochemical detection.A patient was admitted to our hospital due to lower abdominal pain for 1 week.Imaging examination showed right pelvic mass.Laparoscopic exploration revealed a solid mass of 9 cm×8 cm in the right broad ligament.Intraoperative pathology revealed spindle cell tumor with abundant tumor cells.Laparoscopic mass resection,hysterectomy and bilateral salpingectomy were performed.After the postoperative pathological examination,the patient was confirmed as broad ligament PEComa.There was no recurrence after 10 months of operation.

关 键 词：血管周上皮样细胞肿瘤 阔韧带 肿瘤 诊断 治疗 

分 类 号：R730.262[医药卫生—肿瘤]