从肺段浅析Kartagener综合征肺部CT表现及临床特征  

Analysis of CT findings and clinical features of Kartagener syndrome from pulmonary segments

作　　者：刘敬娥 官红莲 兰长青 马晨晖 LIU Jing'e;GUAN Honglian;LAN Changqing;MA Chenhui(Department of Imaging,Fuzhou Pulmonary Hospital,Fuzhou,Fujian 350008,China)

机构地区：[1]福建省福州肺科医院影像科,福州350008

出　　处：《福建医药杂志》2023年第6期16-19,共4页Fujian Medical Journal

摘　　要：目的 总结对Kartagener综合征诊断有提示意义的CT特征及临床表现。方法 收集2007年5月-2021年5月福州肺科医院23例经临床诊断为Kartagener综合征患者的临床及影像资料,将每位患者肺部CT分为18个肺段,总结其中规律。结果 Kartagener综合征肺部支气管扩张具有一定的特异性,本次研究共纳入414个肺段,支气管扩张共累及145个肺段,支气管扩张分型:柱状82段(56.6%)、囊柱状38段(26.2%)、囊状15段(10.3%)、静脉曲张型10段(6.9%);支气管扩张好发位置以中央型为著,并集中于左肺中叶、双肺下叶、右肺舌叶,且常伴随管腔内黏液栓嵌顿和周围细支气管炎症。结论 Kartagener综合征肺部支气管扩张好发于左肺中叶及双肺下叶,以柱状、囊柱状分型为主,常伴副鼻窦气化不良。Objective To summarize the CT features and clinical manifestations suggestive for the diagnosis of Kartagener syndrome.Methods The clinical and imaging data of 23 patients with clinically diagnosed Kartagener syndrome in Fuzhou Pulmonary Hospital from May 2007 to May 2021 were collected.The lung CT of each patient was divided into 18 lung segments,there were a total of 414 lung segments,and the rules were summarized.Results A total of 414 lung segments were included in this study,involving 145 lung segments.The types of bronchiectasis were columnar 82(56.6%),cystic columnar 38(26.2%),cystic 15(10.3%),and varicose 10(6.9%).The most common location of bronchiectasis was the central type,which was concentrated in the left middle lobe of the lung,the lower lobe of both lungs,and the lingual lobe of the right lung.It is often accompanied by mucous thrombectomy in the lumen and inflammation in the surrounding bronchioles.Conclusion The pulmonary bronchiectasis of Kartagener syndrome mainly occurs in the left middle lobe and lower lobe of both lungs,and is mainly characterized by columnar and cystic columnar types,and often accompanied by poor paranasal sinus gasification.

关 键 词：KARTAGENER综合征 纤毛 支气管扩张 计算机断层扫描 

分 类 号：R596[医药卫生—内科学] R562.2[医药卫生—临床医学]