Diseases of bile duct in children  

作　　者：Sutha Eiamkulbutr Chomchanat Tubjareon Anapat Sanpavat Teerasak Phewplung Nimmita Srisan Palittiya Sintusek 

机构地区：[1]Department of Pediatrics,King Chulalongkorn Memorial Hospital,Bangkok 10330,Thailand [2]Department of Pediatrics,Faculty of Medicine,Chulalongkorn University and King Chulalongkorn Memorial Hospital,Bangkok 10330,Thailand [3]Department of Pathology,Chulalongkorn University,Bangkok 10330,Thailand [4]Department of Radiology,Chulalongkorn University,Bangkok 10330,Thailand [5]Department of Surgery,Faculty of Medicine,Chulalongkorn University and King Chulalongkorn Memorial Hospital,Bangkok 10330,Thailand [6]Center of Excellence in Thai Pediatric Gastroenterology,Hepatology and Immunology,Division of Gastroenterology,Department of Pediatrics,King Chulalongkorn Memorial Hospital,Chulalongkorn University,Bangkok 10330,Thailand

出　　处：《World Journal of Gastroenterology》2024年第9期1043-1072,共30页世界胃肠病学杂志（英文版）

基　　金：Ratchadapiseksompotch Fund,Faculty of Medicine,Chulalongkorn University,RA-MF-18/66.

摘　　要：Several diseases originate from bile duct pathology.Despite studies on these diseases,certain etiologies of some of them still cannot be concluded.The most common disease of the bile duct in newborns is biliary atresia,whose prognosis varies according to the age of surgical correction.Other diseases such as Alagille syndrome,inspissated bile duct syndrome,and choledochal cysts are also time-sensitive because they can cause severe liver damage due to obstruction.The majority of these diseases present with cholestatic jaundice in the newborn or infant period,which is quite difficult to differentiate regarding clinical acumen and initial investigations.Intraoperative cholangiography is potentially necessary to make an accurate diagnosis,and further treatment will be performed synchronously or planned as findings suggest.This article provides a concise review of bile duct diseases,with interesting cases.

关 键 词：Bile duct CHOLESTASIS Biliary atresia Biliary hypoplasia Biliary imaging Inspissated bile syndrome Choledochal cyst 

分 类 号：R657.4[医药卫生—外科学] R-332[医药卫生—临床医学]