合并脊髓受累的瘤样原发性中枢神经系统血管炎一例  

Tumor-Like Primary Central Nervous System Vasculitis With Spina Involvement:Report of One Case

作　　者：张莉 孙慧[1] 张世敏 高赛 武雷 黄德晖 ZHANG Li;SUN Hui;ZHANG Shimin;GAO Sai;WU Lei;HUANG Dehui(Department of Neurology,The First Medical Center of Chinese PLA General Hospital,Beijing 100853,China;Department of Neurology,Nanyang First People’s Hospital,Nanyang,Henan 473000,China)

机构地区：[1]中国人民解放军总医院第一医学中心神经内科医学部,北京100853 [2]南阳市第一人民医院神经内科,河南南阳473000

出　　处：《中国医学科学院学报》2024年第3期466-470,共5页Acta Academiae Medicinae Sinicae

摘　　要：原发性中枢神经系统血管炎(PACNS)是一种发生在中枢神经系统的主要侵犯脑、脊髓及软脑膜的中小血管的血管炎性疾病。瘤样PNCAS是PACNS的少见亚型,常被误诊为颅内恶性肿瘤,脊髓受累在PACNS中更为罕见。PACNS因临床症状及影像学表现缺乏特异性,早期诊断困难。本文报道1例经病理确诊合并脊髓受累的瘤样PACNS,以提高对该病的认识。Primary central nervous system vasculitis(PACNS)is a vasculitic disorder affecting small to medium-sized blood vessels primarily in the central nervous system,involving the brain,spinal cord,and meninges.Tumor-like PNCAS,a rare subtype of PACNS,is often misdiagnosed as intracranial malignancy,and that with spinal cord involvement is even more uncommon.The lack of specific clinical symptoms and imaging manifestations poses a challenge to the diagnosis of PACNS.This report presents a case of tumor-like PACNS with spinal cord involvement based on the pathological evidence,aiming to enrich the knowledge about this condition.

关 键 词：原发性中枢神经系统血管炎 脊髓受累 肌电图 

分 类 号：R743[医药卫生—神经病学与精神病学]