Clear cell sarcoma of the pancreas,an unusual cancer with unusual metastatic site or unusual primary site?  

作　　者：Jhenyffer Carvalho Moreno Pedro Luiz Serrano Uson Junior 

机构地区：[1]Universidade 9 de Julho,Sao Paulo 01509120,Brazil [2]Center for Personalized Medicine,Hospital Israelita Albert Einstein,São Paulo 05652900,Brazil [3]Department of Oncology,Hospital do Coração,Sao Paulo 04004030,Brazil

出　　处：《World Journal of Clinical Cases》2024年第25期5653-5656,共4页世界临床病例杂志

摘　　要：Clear cell sarcoma(CCS)is a type of malignant tumor that can arise from tendons and aponeuroses.This malignant proliferation of cells with melanocytic lineage normally occurs in young patients,and it is normally identified in extremities.However,different sites including gastrointestinal organs are also described.Due difficulties in the molecular and histopathology evaluation,the diagnosis is often confused with malignant melanoma.Most cases are treated with surgical resection,but overall,the prognosis is poor.In this editorial,we will discuss a very interesting case of CCS identified in the pancreas.We will discuss the literature and controversies in the management of this type of cancer.Furthermore,we will address molecular strategies to be incorporated in those cases to better understand the primary location of the tumor.Finally,future perspectives of the field and new strategies of treatment will be described.

关 键 词：Clear cell sarcoma Soft tissue sarcoma Metastatic cancer Pancreatic cancer PANCREATECTOMY 

分 类 号：R735.2[医药卫生—肿瘤]