Sclerosing epithelioid fibrosarcoma of the pancreas:A case report  

作　　者：Meng-Qing Sun Li-Na Guo Yan You Yan-Yu Qiu Xiao-Dong He Xian-Lin Han 

机构地区：[1]Department of General Surgery,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences,Beijing 100730,China [2]Department of Pathology,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences,Beijing 100730,China

出　　处：《World Journal of Clinical Cases》2024年第26期5983-5989,共7页世界临床病例杂志

基　　金：Supported by National High Level Hospital Clinical Research Funding,No.2022-PUMCH-B-003;National Multidisciplinary Cooperative Diagnosis and Treatment Capacity Building Project for Major Diseases.

摘　　要：BACKGROUND A sclerosing epithelioid fibrosarcoma(SEF)is a rare malignant fibroblastic soft tissue tumor that rarely occurs in intra-abdominal organs.A case of a SEF in the pancreatic head is reported herein,including its clinical manifestations,preoperative imaging features,gross specimen and pathological findings.CASE SUMMARY A 33-year-old male patient was admitted to Peking Union Medical College Hospital in December 2023 due to a one-year history of intermittent upper abdominal pain and the discovery of a pancreatic mass.The patient underwent an enhanced computed tomography scan of the abdomen,which revealed a welldefined,round mass with clear borders and calcifications in the pancreatic head.The mass exhibited progressive,uneven mild enhancement,measuring approximately 6.6 cm×6.3 cm.The patient underwent laparoscopic pylorus-preserving pancreaticoduodenectomy.Postoperative pathological examination revealed that the lesion was consistent with a SEF.At the 3-month postoperative follow-up,the patient did not report any short-term complications,and there were no signs of tumor recurrence.CONCLUSION SEFs are rare malignant fibrous soft tissue tumors.SEFs rarely develop in the pancreas,and its preoperative diagnosis depends on imaging findings,with confirmation depending on pathological examination and immunohistochemistry.Currently,only four cases of pancreatic SEF have been reported in studies written in English.This case is the first reported case of a pancreatic SEF by a clinical physician.

关 键 词：Sclerosing epithelioid fibrosarcoma of the pancreas Abdominal malignant fibroblastic soft tissue tumor Abdominal enhanced computed tomography Laparoscopic pancreaticoduodenectomy Case report 

分 类 号：R73[医药卫生—肿瘤] R576[医药卫生—临床医学]