病例分析:1例Carney三联征的影像学表现  

Imaging features of Carney triad:a case analysis

作　　者：胡肃 王永芹[2] 旦增卓嘎 尹源[3] 李峥艳[1] 袁放[1] 刘曦娇[1,4] 黄子星 宋彬[1,4] HU Su;WANG Yongqin;Danzengzhuoga;YIN Yuan;LI Zhengyan;YUAN Fang;LIU Xijiao;HUANG Zixing;SONG Bin(Department of Radiology,West China Hospital,Sichuan University,Chengdu 610041,P.R.China;Affiliated Hospital of Chengdu University,Chengdu 610081,P.R.China;Gastric Cancer Center,West China Hospital,Sichuan University,Chengdu 610041,P.R.China;Department of Radiology,Sanya People’s Hospital,Sanya,Hainan 572000,P.R.China)

机构地区：[1]四川大学华西医院放射科,成都610041 [2]成都大学附属医院,成都610081 [3]四川大学华西医院胃癌中心,成都610041 [4]三亚市人民医院放射科,海南三亚572000

出　　处：《中国普外基础与临床杂志》2024年第7期810-814,共5页Chinese Journal of Bases and Clinics In General Surgery

基　　金：国家自然科学基金(项目编号:82001810);四川省自然科学基金面上项目(项目编号:2022NSFSC0840);四川省区域创新合作重点研发项目(项目编号:2022YFQ0095)。

摘　　要：Carney三联征是一种罕见的肿瘤综合征,相关报道较少。现向读者展示1例罕见的年轻女性Carney三联征(含胃间质瘤、肾细胞癌、左肾上腺嗜铬细胞瘤及肺软骨瘤)的增强CT及MRI图像,旨在为此病的临床诊断及鉴别诊断提供参考。通过本病例提醒影像诊断医师及临床医师,在有原发性胃肠间质瘤的病史下,特定部位发生的肿瘤性病变(肺软骨瘤、左肾上腺嗜铬细胞瘤、肾细胞癌等),需警惕合并Carney三联征的可能。Carney triad is a rare tumor syndrome with few reports.This case showed the enhanced CT and MRI images of a rare young woman patient with Carney triad(containing gastric stromal tumor,renal cell carcinoma,adrenal pheochromocytoma,and pulmonary chondrosarcoma),which is intended to provide a reference for clinical diagnosis and differential diagnosis.This case reminds the radiologists and clinicians that the patients with a history of primary gastrointestinal stromal tumor and neoplastic lesions occurring at specific sites(pulmonary chondrosarcoma,adrenal pheochromocytoma,renal cell carcinoma,etc.)need to be alerted to the possibility of combining with Carney triad.

关 键 词：Carney三联征 胃肠间质瘤 肾细胞癌 嗜铬细胞瘤 肺软骨瘤 影像征象 

分 类 号：R730[医药卫生—肿瘤]