常见原发性皮肤T细胞淋巴瘤诊疗中国专家共识(2024年版)  

Chinese expert consensus on common primary cutaneous T-cell lymphoma (2024 version)

作　　者：中国临床肿瘤学会(CSCO)淋巴瘤专家委员会 马军[2] 朱军 赵东陆[4] Lymphoma Expert Committee of Chinese Society of Clinical Oncology(CSco);Ma Jun(不详;Harbin Institute of Hematology and Oncology,Harbin 150010)

机构地区：[1]不详 [2]哈尔滨血液病肿瘤研究所,哈尔滨150010 [3]北京大学肿瘤医院 [4]哈尔滨血液病肿瘤研究所

出　　处：《白血病．淋巴瘤》2024年第6期321-328,共8页Journal of Leukemia & Lymphoma

摘　　要：原发性皮肤T细胞淋巴瘤(PCTCL)是一组原发于皮肤的罕见非霍奇金淋巴瘤, 最常见亚型为蕈样肉芽肿, 其次为原发性皮肤CD30阳性T细胞淋巴组织增生性疾病。虽然2022年第5版世界卫生组织造血淋巴肿瘤分类已将Sézary综合征从PCTCL中划除, 但基于其与蕈样肉芽肿的密切相关性, 依然有必要一起讨论。PCTCL的早期确诊和及时治疗十分重要, 专家组成员结合PCTCL的诊治现状及国内外相关研究数据, 制定了该共识, 旨在为临床医生提供参考。Primary cutaneous T-cell lymphoma(PCTCL)is a group of rare non-Hodgkin lymphomas that originate in the skin.The most common subtype is mycosis fungoides,followed by primary cutaneous CD30-positive T-cell lymphoproliferative disorders.Although Sézary syndrome has been excluded from primary cutaneous T-cell lymphomas in the 5th edition of World Health Organization classification of haematolymphoid tumours,it is still necessary to discuss it due to its close association with mycosis fungoides.Early diagnosis and timely treatment of primary cutaneous T-cell lymphoma are crucial.The members of the expert group formulate the consensus by combining the current status of diagnosis and treatment of PCTCL and relevant research data at home and abroad,which aims to provide references for clinicians.

关 键 词：淋巴瘤 T细胞 皮肤 蕈样肉芽肿 淋巴瘤 原发性皮肤间变性大细胞 SÉZARY综合征 淋巴瘤样丘疹病 

分 类 号：R739.5[医药卫生—肿瘤]