一例罕见巨大多囊肝并多囊肾肝移植术后病例报道并治疗进展  

One Rare Case after Giant Polycystic Liver and Polycystic Kidney Liver Transplantation Was Reported and Treatment Progressed

作　　者：刘瑞 胡明利 杨胜波 LIU Rui;HU Ming-li;YANG Sheng-bo(The Second Clinical College of Guizhou University of Traditional Chinese Medicine,Guiyang 550000,Guizhou Province,China;Department of Hepatobiliary,Pancreatic,and Spleen Surgery,The Second Affiliated Hospital of Guizhou University of Traditional Chinese Medicine,Guiyang 550000,Guizhou Province,China)

机构地区：[1]贵州中医药大学第二临床学院,贵州贵阳550000 [2]贵州省中医药大学第二附属医院肝胆胰脾外科,贵州贵阳550000

出　　处：《罕少疾病杂志》2024年第8期1-2,共2页Journal of Rare and Uncommon Diseases

基　　金：贵州省中医院管理局;民族医药科学技术研究课题研究(QZYY2017-10)。

摘　　要：目的目前国内对罕见巨大多囊肝并多囊肾肝移植术后病例报道较少,本文通过分析总结治疗1例罕见巨大多囊肝并多囊肾肝移植术后患者的经验,对该病的治疗进展以及临床治疗提供借鉴与建议。方法将我院1例罕见巨大多囊肝并多囊肾肝移植术后患者的诊断、治疗等过程与国内外相关报道进行对比,查阅相关文献,结合此例患者的临床情况以及影像学表现,探讨对多囊性肝疾病的临床诊疗方法。结果患者在行肝移植后,病情得到改善。结论肝移植、肾移植仍是目前该病的唯一根治手段,TAE治疗可作为辅助治疗手段。对于GigotⅠ、Ⅱ期患者,可使用生长抑素类似物延缓或停止该病进展;对于GigotⅢ期患者,可先使用生长抑素类似物延减小肝囊肿体积,待达到肝部分切除术手术指标后再行肝部分切除。Objective At present,there are few cases of rare giant polycystic liver and polycystic kidney liver transplantation in China,and this article summarizes the experience of treating one patient after rare giant polycystic liver and polycystic kidney liver transplantation,and provides reference and suggestions for the treatment progress and clinical treatment of this disease.Methods The diagnosis and treatment of a rare patient with giant polycystic liver and polycystic kidney liver transplantation in our hospital was compared with relevant reports at home and abroad,relevant literature was reviewed,and the clinical diagnosis and treatment methods of polycystic liver disease were discussed based on the clinical situation and imaging manifestations of this patient.Results The patient's condition improved after liver transplantation.Conclusion Liver transplantation and kidney transplantation are still the only radical treatment methods for this disease,TAE therapy can be used as an adjunct treatment.In patients with Gigot stageⅠandⅡ,somatostatin analogues can be used to delay or stop progression;For patients with stageⅢGiget,somatostatin analogues can be used to reduce the size of the liver cyst first,and then perform partial liver resection after the surgical target of partial hepatic resection is reached.

关 键 词：多囊肝 多囊肾 肝移植 病例报告 

分 类 号：R392.4[医药卫生—免疫学]