会阴部侵袭性血管黏液瘤1例报告并文献复习  

Aggressive angiomyxoma of the perineum:a case report and literature review

作　　者：黄高振 刘凯锋 孙蕊旭 唐泉青 刘宏伟 Huang Gaozhen;Liu Kaifeng;Sun Ruixu;Tang Quanqing;Liu Hongwei(Department of Urology,Laboratory of Urology,Affiliated Hospital of Guangdong Medical University,Zhanjiang 524001,Guangdong,China)

机构地区：[1]广东医科大学附属医院泌尿外科,泌尿外科研究室,广东湛江524001

出　　处：《中国男科学杂志》2024年第5期76-82,共7页Chinese Journal of Andrology

基　　金：广东省基础与应用基础研究基金(2024A1515012742)。

摘　　要：目的探讨会阴部侵袭性血管黏液瘤的临床特点、诊疗现状及预后,以期提高临床医师对该疾病的认识。方法回顾性分析本院2023年11月收治的1例男性会阴部侵袭性血管黏液瘤的辅助检查及病理结果,并结合文献复习。结果本例患者有会阴部胀痛表现。磁共振成像考虑间质来源偏恶性肿瘤可能性大。予行会阴部肿物切除术,术后病理提示侵袭性血管黏液瘤,术后随访4个月未见复发。分析31例盆腔、会阴部及腹股沟侵袭性血管黏液瘤患者的文献资料,其中女性24例,男性7例,发病时间从3周到12年不等,大部分患者无特殊临床症状。所有患者均行手术治疗,其中10例术后予辅助治疗。随访发现3例患者术后复发。结论会阴部侵袭性血管黏液瘤是一种罕见的软组织肿瘤,主要表现为会阴部胀痛不适。确诊通常需要依赖病理学检查,主要治疗方式为手术完整切除,术后需长期随访。Objective To explore the clinical features,current status of diagnosis and treatment,and prognosis of aggressive angiomyxoma(AAM)of the perineum,to improve clinicians'understanding of this disease.Methods We retrospectively analyzed the ancillary examination and pathological results of a case of male perineal AAM admitted to our hospital in November 2023,and reviewed the literature.Results The patient presented with perineal distension and pain.The results of magnetic resonance imaging suggested that the tumor was more likely to be a malignant tumor from the stroma.Perineal mass resection was performed,postoperative pathology suggested AAM,and no recurrence was found after 4 months of follow-up.The literature of 31 patients with pelvic,perineal and inguinal AAM were analyzed,including 24 females and 7 males.The onset time ranged from 3 weeks to 12 years.Most patients had no special clinical symptoms.All patients underwent surgical treatment and 10 of them were given adjuvant treatment after surgery.The follow-up showed that 3 patients had postoperative recurrenc.Conclusion Perineal AAM is a rare soft tissue tumor,mainly manifested as perineal pain and discomfort.Confirmation of the diagnosis usually relies on pathologic examination,and the main treatment is complete surgical excision and long-term follow-up.

关 键 词：会阴部侵袭性血管黏液瘤 会阴部肿瘤 盆腔肿瘤 软组织肿瘤 

分 类 号：R738.6[医药卫生—肿瘤]