肺毛细血管瘤病1例  

Pulmonary capillary hemangiomatosis:a case report

作　　者：张英为[1] 俞砚喆[1] 邱玉英[1] 刘小琴[1] 程乐[2] 徐新运[3] 孟凡青[3] 蔡后荣[1] Zhang Yingwei;Yu Yanzhe;Qiu Yuying;Liu Xiaoqin;Cheng Le;Xu Xinyun;Meng Fanqing;Cai Hourong(Department of Pulmonary and Critical Care Medicine,Nanjing Drum Tower Hospital,Affiliated Hospital of Medical School,Nanjing University,Nanjing 210008,China;Department of Radiology,Nanjing Drum Tower Hospital,Affiliated Hospital of Medical School,Nanjing University,Nanjing 210008,China;Department of Pathology,Nanjing Drum Tower Hospital,Afiliated Hospital of Medical School,Nanjing University,Nanjing 210008,China)

机构地区：[1]南京大学医学院附属鼓楼医院呼吸与危重症医学科,南京210008 [2]南京大学医学院附属鼓楼医院影像科,南京210008 [3]南京大学医学院附属鼓楼医院病理科,南京210008

出　　处：《中华结核和呼吸杂志》2024年第12期1144-1147,共4页Chinese Journal of Tuberculosis and Respiratory Diseases

摘　　要：肺毛细血管瘤病(PCH)是一种罕见的肺血管疾病,发病率为4/100万,以肺动脉高压为特征,临床病程缓慢,除了胸闷、气短、呼吸困难之外,少数患者还可以表现为反复或频繁咯血及胸痛等。本文介绍1例外院诊断为过敏性肺炎患者,入院后经过胸腔镜肺活检最终诊断为PCH的病例,旨在提高临床医生对该病诊断意识和诊疗水平。Pulmonary capillary hemangiomatosis(PCH)is a rare pulmonary vascular disorder with a prevalence of approximately 4 cases per million individuals.It is characterized by pulmonary hypertension leading to symptoms of shortness of breath and dyspnea,and rarely hemoptysis or chest pain.This manuscript reported a case of PCH that was initially misdiagnosed as hypersensitive pneumonitis and was finally confirmed by thoracoscopic lung biopsy.The aim of this report was to increase diagnostic awareness and improve the management of this disease.

关 键 词：肺毛细血管 过敏性肺炎 临床病程 肺血管疾病 瘤病 临床医生 诊断意识 胸痛 

分 类 号：R734.2[医药卫生—肿瘤]