儿童血管瘤样纤维组织细胞瘤影像学表现  

Imaging Features of Angiomatoid Fibrous Histiocytoma in Children

作　　者：张欢欢[1] 李婷婷 杨秀军 徐蓉 ZHANG Huanhuan;LI Tingting;YANG Xiujun(Department of Radiology,Shanghai Children’s Hospital,School of medicine,Shanghai Jiao Tong University,Shanghai 200062,P.R.China)

机构地区：[1]上海市儿童医院,上海交通大学医学院附属儿童医院影像科,200062

出　　处：《临床放射学杂志》2025年第4期707-712,共6页Journal of Clinical Radiology

摘　　要：目的 探讨儿童血管瘤样纤维组织细胞瘤(AFH)的影像学特征及诊断要点,为其早期诊断提供参考。方法 搜集并回顾性分析经手术病理证实的7例AFH临床及影像资料,结合文献,总结、分析其CT、MRI及超声表现。结果 男2例、女5例,年龄4个月~11岁,中位年龄8岁。1例伴有皮肤破溃出血,3例伴发热、贫血、血常规异常等全身炎症反应。7例AFH均为单发病变,其中位于上肢5例、腹部1例、肺1例。上肢和腹部病变表现为边界清的囊实性或实性肿块,增强扫描实性部分明显强化,部分病变内可见钙化、出血及强化血管;肺部病变表现为边界清的孤立性结节,增强扫描呈持续性强化。囊实性病变伴出血、包膜征、强化血管等征象对该病有一定提示。结论 儿童AFH影像学表现具有一定的特征性和多样性,应结合临床、影像学表现全面认识和综合分析,减少误诊。Objective To explore the imaging features of angiomatoid fibrous histiocytoma(AFH) in children and to provide reference for its early diagnosis.Methods We retrospectively analyzed the clinical and imaging characteristics of 7 cases of AFH confirmed by pathology,and summarized and analyzed the CT,MRI and ultrasound features.Results The 7 patients included 2 boys and 4 girls,aged from 4 months to 11 years,with a median age of 5 years.One case was accompanied by skin breakdown and bleeding,and 3 caseswere accompanied by systemic inflammatory reactions,such as fever,anemia,and abnormal blood counts.All 7 cases were single lesions.The affected areas included 5 cases in the upper limbs,1 case in the abdomen,and 1 case in the lungs.The lesions in the upper limbs and abdomen showed clear cystic solid or mass with obvious enhancement of the mass part,and calcification,hemorrhage and focal enhancement were seen occasionally.The lesions in the lungs showed clear isolated nodularwithpersistent contrast enhancement.The signs of cystic lesions,hemorrhage,fibrous membrane,and focal enhancement were suggestive.Conclusion AFH in children has varied imaging features,but some specific features still exist.Combining clinical and imaging findings to recognize and analyze comprehensively is helpful to reduce misdiagnosis.

关 键 词：血管瘤样纤维组织细胞瘤 儿童 体层摄影术 X线计算机 磁共振成像 超声表现 

分 类 号：R73[医药卫生—肿瘤]