超长节段脊髓及脑膜强化的自身免疫性胶质纤维酸性蛋白星形细胞病一例  

Autoimmune Glial Fibrillary Acid Protein Astrocytopathy with Hyper-Long Segmental Spinal Cord and Meningeal Enhancement: A Case Report

作　　者：金桐羽 司志华[2] 王爱华[1,2] 

机构地区：[1]山东大学,山东 济南 [2]山东省千佛山医院神经病学科,山东 济南

出　　处：《临床医学进展》2022年第12期11921-11927,共7页Advances in Clinical Medicine

摘　　要：自身免疫性胶质纤维酸性蛋白星形细胞病(Autoimmune glial fibrillary acidic protein Astrocytopathy, GFAP-A)是一组累及脑膜、脑、脊髓、视神经及不同部位组合的综合征,该病由梅奥诊所于2016年首先命名并报道。本文报道一例同时出现超长节段脊髓(延髓-T12)和明显脑膜、侧脑室旁强化,且合并罕见贲门腺癌的病例。Autoimmune glial fibrillary acid protein astrocytoma (GFAP-A) is a group of syndromes involving the meninges, brain, spinal cord, optic nerve, and various combinations of sites. The disease was first reported and named by the Mayo Clinic in 2016. This paper reports a case of extra-long seg-mental spinal cord (medulla oblongata-T12) and marked meningeal and lateral paraventricular enhancement with rare cardia adenocarcinoma.

关 键 词：自身免疫性胶质纤维酸性蛋白星形细胞病 脑膜炎 脑脊髓炎 贲门腺癌 

分 类 号：R739.45[医药卫生—肿瘤]