自身免疫性肝炎–原发性胆汁性胆管炎重叠综合征合并干燥综合征1例报告  

Autoimmune Hepatitis-Primary Biliary Cholangitis Overlap Syndrome with Sjögren Syndrome: A Case Report

作　　者：邹沛炫 黄卫[1] 

机构地区：[1]暨南大学附属第一医院消化内科,广东 广州

出　　处：《临床医学进展》2025年第3期1752-1759,共8页Advances in Clinical Medicine

摘　　要：原发性胆汁性肝硬化(Primary Biliary Cholangitis, PBC)和自身免疫性肝炎(Autoimmune Hepatitis, AIH)是不同的自身免疫性慢性肝病,这2种疾病在同一患者中共存称为重叠综合征。干燥综合征(Sjögren Syndrome, SS)是自身免疫性肝病(Autoimmune Liver Disease, AILD)最常并发的肝外自身免疫病。本文报告了一例AIH-PBC重叠综合征合并SS的病例,探讨其临床表现、诊断和治疗策略。Autoimmune hepatitis (AIH) and primary biliary cholangitis (PBC) are two common clinical autoimmune liver diseases, and some patients have both diseases;this feature is called AIH-PBC overlap syndrome. Sjögren syndrome is one of the most common extrahepatic autoimmune diseases among patients with autoimmune liver diseases. This article presents the case report of an elderly female patient who was diagnosed with AIH-PBC overlap syndrome combined with Sjögren syndrome, and discusses its clinical presentation, diagnosis and treatment strategies.

关 键 词：自身免疫性肝病 AIH-PBC重叠综合征 干燥综合征 病例报告 

分 类 号：R575[医药卫生—消化系统]