多形性透明变性血管扩张瘤一例  

One Case: Pleomorphic Hyalinizing Angiectatic Tumor

作　　者：张烨 熊玉超 黄俊斌 李志琼 王博焕 曾旭文[1] 

机构地区：[1]暨南大学附属广州红十字会医院(广州市应急医院),放射科,广东 广州

出　　处：《医学诊断》2024年第4期401-406,共6页Medical Diagnosis

摘　　要：多形性透明变性血管扩张瘤(PHAT)是由Smith等人在1996年提出的一种罕见的低级别间叶源性肿瘤。WHO在2020年将其归类于分化未定的低度恶性肿瘤。组织学上PHAT的显着特征是存在扩张血管簇、条索状分布于扩张性血管之间的梭形和圆形瘤细胞及血管壁、血管周围及瘤细胞之间基质明显透明样变性。现报告我院1例大腿多形性透明变性血管扩张瘤患者,并分析此例患者的相关资料,汇总临床、影像及病理特点。病例男,56岁。发现左大腿内侧皮下肿物4年,近1年来自觉肿块较前明显增大。Pleomorphic hyalinizing angiectatic tumor (PHAT) is a rare low grade mesenchymal origin tumour proposed by Smith et al. in 1996. WHO classified it as a low grade malignant tumour with undifferentiated differentiation in 2020. Histologically the distinguishing features of PHAT are the presence of clusters of dilated blood vessels, strips of spindle shaped and rounded tumour cells distributed between dilated blood vessels and marked hyaline-like degeneration of the vascular wall, perivascular area and stroma between tumour cells. We report a case of pleomorphic hyaline degenerative angiodysplasia of the thigh in our hospital, and analyse the relevant data of this patient, summarizing the clinical, imaging and pathological features. The case was a 56-year-old man. A subcutaneous mass was found in the left inner thigh for 4 years, and in the past 1 year, the mass had increased significantly compared with the previous one.

关 键 词：软组织 多形性透明变性血管扩张性肿瘤 体层摄影术 磁共振成像 

分 类 号：R73[医药卫生—肿瘤]