Late Discovery of a Vein of Galen Aneurysmal Malformation Complicated with Hydrocephalus: A Case Report  

作　　者：Diop Abdoulaye Faye Mohameth Cissé Mohamed El Hassimi Thioub Mbaye Ba Momar Code Badiane Seydou Boubakar 

机构地区：[1]Neurosurgery Department of CHNU Fann, Dakar, Senegal

出　　处：《Open Journal of Modern Neurosurgery》2020年第2期254-259,共6页现代神经外科学进展（英文）

摘　　要：The aneurysmal malformation of the vein of Galen is a rare condition, corresponding to less than 1% of intracranial vascular malformations. It is a disease affecting mainly newborns and small children. We are reporting the case of an 11-year-old teenager who presented consciousness disorders associated to generalized convulsive seizures. The cerebral CT scan supplemented by an angioscanner, revealed an important expansive process in the pineal region, confirming the diagnosis of an aneurysmal malformation of the Galen’s ampulla with upstream obstructive hydrocephalus. The child benefited from a ventriculo-peritoneal shunt with favorable immediate operative sequels. His death occurred at home two months after surgery over the course of a convulsive seizure with post critical coma.The aneurysmal malformation of the vein of Galen is a rare condition, corresponding to less than 1% of intracranial vascular malformations. It is a disease affecting mainly newborns and small children. We are reporting the case of an 11-year-old teenager who presented consciousness disorders associated to generalized convulsive seizures. The cerebral CT scan supplemented by an angioscanner, revealed an important expansive process in the pineal region, confirming the diagnosis of an aneurysmal malformation of the Galen’s ampulla with upstream obstructive hydrocephalus. The child benefited from a ventriculo-peritoneal shunt with favorable immediate operative sequels. His death occurred at home two months after surgery over the course of a convulsive seizure with post critical coma.

关 键 词：INTRACRANIAL Vascular MALFORMATION ARTERIOVENOUS MALFORMATION Vein of GALEN 

分 类 号：R74[医药卫生—神经病学与精神病学]