Angioid Streaks in Psuedoxanthoma Elasticum  

作　　者：Mehrdad Mohammadpour Nazanin Ebrahimiadib Seyed Ali Tabatabaei Mohammad Soleimani Shima Dehghani Fatemeh Abdi Ghasem Saeedi Anari Amir Hasan Matini Mahyar Noorbakhsh Zahra Ghomi 

机构地区：[1]Eye Research Center, Farabi Eye Hospital, Tehran University of Medical Sciences, Tehran, Iran [2]Shahid Beheshti Hospital, Kashan University of Medical Sciences, Kashan, Iran

出　　处：《Open Journal of Ophthalmology》2017年第1期57-63,共7页眼科学期刊（英文）

摘　　要：Pseudoxanthoma elasticum (PXE) is a hereditary disorder that affects primarily the elastic tissues of skin, eyes and blood vessels. Its estimated prevalence is thought to be 1:25,000 - 100,000. PXE patients also carry an increased risk for cardiovascular and gastrointestinal diseases. Early diagnosis can play a crucial role in preventing early loss of vision and systemic complications in these patients however despite having characteristic clinical features;it is still to a large extent being under-diagnosed. Here we present two cases of PXE with reduced vision.Pseudoxanthoma elasticum (PXE) is a hereditary disorder that affects primarily the elastic tissues of skin, eyes and blood vessels. Its estimated prevalence is thought to be 1:25,000 - 100,000. PXE patients also carry an increased risk for cardiovascular and gastrointestinal diseases. Early diagnosis can play a crucial role in preventing early loss of vision and systemic complications in these patients however despite having characteristic clinical features;it is still to a large extent being under-diagnosed. Here we present two cases of PXE with reduced vision.

关 键 词：Pseudoxanthoma Elasticum (PXE) Angioid STREAKS DRUSEN 

分 类 号：R73[医药卫生—肿瘤]