Heart Disease Scleroderma Revelators: About a Clinical Case  

作　　者：Coumba Thiam Boubacar Sonfo Youssouf Camara Asmaou Keita Mariam Sako Békaye Traoré Djeneba Koné Mamadou Touré Massama Konaté Hamidou Oumar Bâ Ibrahima Sangaré Sanoussi Daffe Daouda Fofana Mariam Cheick Traoré Boureima Dembélé Boubacar Diarra Hamidou Camara Samba Sidibé Souleymane Coulibaly Ichaka Menta Ousmane Faye Coumba Thiam;Boubacar Sonfo;Youssouf Camara;Asmaou Keita;Mariam Sako;Békaye Traoré;Djeneba Koné;Mamadou Touré;Massama Konaté;Hamidou Oumar Bâ;Ibrahima Sangaré;Sanoussi Daffe;Daouda Fofana;Mariam Cheick Traoré;Boureima Dembélé;Boubacar Diarra;Hamidou Camara;Samba Sidibé;Souleymane Coulibaly;Ichaka Menta;Ousmane Faye(Department of Cardiology, Kati University Hospital, Kati, Mali;Department of Cardiology, The Mother-Child University Hospital, Bamako, Mali;Department of Cardiology, CHU Point G, Bamako, Mali;Department of Cardiology, The CHU Gabriel Touré, Bamako, Mali;Dermatology Hospital of Bamako, Bamako, Mali;Department of Internal Medicine, Mali Hospital, Bamako, Mali)

机构地区：[1]Department of Cardiology, Kati University Hospital, Kati, Mali [2]Department of Cardiology, The Mother-Child University Hospital, Bamako, Mali [3]Department of Cardiology, CHU Point G, Bamako, Mali [4]Department of Cardiology, The CHU Gabriel Touré, Bamako, Mali [5]Dermatology Hospital of Bamako, Bamako, Mali [6]Department of Internal Medicine, Mali Hospital, Bamako, Mali

出　　处：《World Journal of Cardiovascular Diseases》2023年第9期578-585,共8页心血管病（英文）

摘　　要：Scleroderma (or systemic sclerosis) is a disease characterized by abnormalities in the functioning of small blood vessels and the immune system, ultimately leading to inflammation and excessive fibrosis of the skin and various organs, including the heart. Management must be multidisciplinary, to avoid complications that are often serious. We report the case of a 20-year-old patient with no known cardiovascular history who consults for dyspnea, and retrosternal pain associated with a dry cough. On physical examination, she had tachycardia, swelling of the lower limbs, jugular turgidity, and deafening heart sounds. Cardiac Doppler ultrasound shows dilation of the right cavities, paradoxical septum and significant pulmonary arterial hypertension, pericardial effusion of medium abundance. On oral examination, it presents an ulceration of the lips, dermatological examination finds scattered hypo chromic spots in the body, more accentuated in the face. Before the hypo chromic dermatosis, a dermatological consultation was carried out with an autoimmune assessment that came back positive for systemic scleroderma.Scleroderma (or systemic sclerosis) is a disease characterized by abnormalities in the functioning of small blood vessels and the immune system, ultimately leading to inflammation and excessive fibrosis of the skin and various organs, including the heart. Management must be multidisciplinary, to avoid complications that are often serious. We report the case of a 20-year-old patient with no known cardiovascular history who consults for dyspnea, and retrosternal pain associated with a dry cough. On physical examination, she had tachycardia, swelling of the lower limbs, jugular turgidity, and deafening heart sounds. Cardiac Doppler ultrasound shows dilation of the right cavities, paradoxical septum and significant pulmonary arterial hypertension, pericardial effusion of medium abundance. On oral examination, it presents an ulceration of the lips, dermatological examination finds scattered hypo chromic spots in the body, more accentuated in the face. Before the hypo chromic dermatosis, a dermatological consultation was carried out with an autoimmune assessment that came back positive for systemic scleroderma.

关 键 词：Heart Failure SCLERODERMA Young Subject 

分 类 号：R54[医药卫生—心血管疾病]