Isolated cervical extraosseous intradural chordoma attached to the C5 nerve root: a case report  

作　　者：Juliana Rotter Kyle Mueller Ashley MacConnell Jason McGowan Steven Spitz 

机构地区：[1]Georgetown University School of Medicine,3700 Reservoir Rd,Washington,DC 20007,USA [2]Department of Neurosurgery,Medstar Georgetown University Hospital,3800 Reservoir Rd,Washington,DC 20007,USA [3]Department of Neurosurgery,University of Pittsburgh Medical Center,200 Lothrop St.Ste B400,Pittsburg,PA 15213,USA

出　　处：《Chinese Neurosurgical Journal》2019年第4期242-245,共4页中华神经外科杂志（英文）

摘　　要：Background:As chordomas are slow growing and locally invasive with high recurrence rates,initial recommendations include complete surgical resection with or without radiation therapy.A large proportion of recurrences occur years after initial resection necessitating lengthy follow-up.The novel biomarker brachyury and the repurposing of pharmaceutical products have the potential to substantially impact long-term recurrence rates.Case presentation:A 43-year-old woman presented with an isolated,cervical extraosseous intradural extramedullary chordoma attached to a nerve root underwent a C3-5 laminectomy,C3-5 lateral mass screw instrumentation,and mass resection.All symptoms resolved by the 12-month postoperative follow-up visit.Conclusions:This is the first report of an isolated,cervical extraosseous intradural extramedullary chordoma attached to a nerve root,and this case adds to the previous six TypeⅣchordomas in the literature.Unfortunately,the very rare form of extraosseous intradural chordoma is poorly understood:the lack of detailed knowledge in how they are differentiated from other forms of chordoma confounds the development of optimal treatment strategies and follow-up guidelines.

关 键 词：CHORDOMA EXTRAOSSEOUS Nerve root CERVICAL spine INTRADURAL EXTRAMEDULLARY 

分 类 号：R73[医药卫生—肿瘤]