进行性肌营养不良患儿的临床及肌电图分析  

Clinical and electromyographic analysis of progressive muscular dystrophy in children

作　　者：刘敏[1] 石靖[1] 

机构地区：[1]广西医科大学第一附属医院儿一科,广西南宁530021

出　　处：《临床神经电生理学杂志》2008年第6期340-342,共3页Journal of Clinical Electroneurophysiology

摘　　要：目的:探讨进行性肌营养不良(PMD)患儿的临床和肌电图特点。方法:回顾性分析35例进行性肌营养不良患儿的临床和肌电图资料。结果:35例PMD患儿中,Duchenne型肌营养不良型占85.7%,出现进行性加重的四肢肌无力和萎缩,血清肌酸激酶(CK)明显增高,肌电图显示自发电位的出现率为21.4%,轻用力时均出现短时限、低波幅的运动单位电位,神经传导速度大致正常。结论:PMD的诊断及分型应依据临床特点、肌电图及肌活检结果综合分析。Objective:To explore the features of clinic and electromyography in children with progressive muscular dystrophy. Methods: The clinical features and laboratory data were analyzed in 35 children with progressive muscular dystrophy and electromyography tests were carried out. Results: Duchenne muscular dystrophy took up 30 cases(85.7%)in 35 patients.Children were characterized by progressive symmetrical weakness of proximal limbs and muscular atrophy. The level of creatine kinase(CK)in serum was significantly...

关 键 词：肌营养不良 儿童 肌电图 肌活检 

分 类 号：R746.2[医药卫生—神经病学与精神病学]