颅面血管瘤病  

Encephalofacial angiomatosis

作　　者：焦德让[1] 只达石[2] 卫启明[1] 姚鑫[1] 刘暌[1] 秦进喜[3] 王实[1] 

机构地区：[1]天津市环湖医院神经外科,300060 [2]天津医科大学总医院 [3]天津市环湖医院神病理科,300060

出　　处：《中国现代神经疾病杂志》2004年第1期30-35,共6页Chinese Journal of Contemporary Neurology and Neurosurgery

摘　　要：目的探讨颅面血管瘤病的病理改变及治疗原则。方法回顾分析1980年1月～1995年12月治疗的7例(男1例,女6例)颅面血管瘤病患者的病理改变及手术治疗结果。其中Ⅰ型4例,Ⅱ型2例,Ⅲ型1例,主要临床表现为面部血管痣、癫痫发作、智力障碍以及偏瘫;脑电图检查显示病变部位异常脑电波。结果7例患者中除1例死亡外,其余6例手术后临床症状及脑电图均有不同程度改善。病理改变包括颅骨不对称,颅内钙化,脑萎缩,脑室扩大,硬脑膜和蛛网膜血管扩张、增生及脑血管扩张,静脉畸形等。结论对于药物控制不满意的颅面血管瘤病患者,可考虑手术治疗。Objective To study the pathological changes and therapeutic principles in encephalofacial angiomatosis. Methods The pathological changes and surgical effects of 7 patients (male 1 female 6) with encephalofacial angiomatosis in this hospital during January 1980 to December 1995 were retrospectively analyzed. There were type Ⅰ(n=4), type Ⅱ(n=2) and type Ⅲ (n=1) in these patients. Their main clinical manifestations were facial nevus vascularis, epileptic attack, dysnoesia and hemiplegia. Abnormal EEG was showed in the site of angioma. Results The clinical symptoms and EEG patterns were improved in different extent postoperatively in all of these patients except 1 death. Pathological changes of the patients included asymmetric calvarium, intracranial calcification, cerebral atrophy, ventricular enlargement, vascular dilation and hyperplasia of dura and arachnoid, cerebral venous malformation etc. Conclusion Surgical treatment may be the choice for patients while drug control is unsatisfactory.

关 键 词：颅面 血管瘤 病理改变 患者 手术治疗 血管扩张 静脉畸形 颅内钙化 脑室扩大 血管痣 

分 类 号：R739.4[医药卫生—肿瘤]