双肾多发性错构瘤合并结节性硬化3例分析  

The diagnosis and treatment of bilateral multifocal renal angiomyolipomas in patients with tuberous sclerosis

作　　者：刘尚文[1] 周大庆[1] 李文刚[1] 

机构地区：[1]解放军303医院泌尿外科,南宁市530000

出　　处：《实用医学杂志》2008年第20期3522-3523,共2页The Journal of Practical Medicine

摘　　要：目的:提高双肾多发性错构瘤合并结节性硬化的诊断与治疗水平。方法:对3例双肾多发性错构瘤合并结节性硬化患者的临床资料和随访情况进行回顾性分析。结果:1例患者接受单侧肾切除手术治疗,术后10d死于多器官功能衰竭,2例随访24个月病情无进展。结论:双肾多发性错构瘤合并结节性硬化患者在无症状期,应严格观察,手术治疗应慎重,在症状进展较快时,选择性动脉栓塞为首选。Objective To evaluate the diagnosis and treatment of bilateral multifocal renal angiomyolipomas in patients with tuberous sclerosis. Methods Three cases of bilateral muhifocal renal angiomyolipomas accompanied by tuberous sclerosis were analyzed retrospectively. Results One case undergoing nephrectomy died 10 days later for multiple organ failure; two patients with renal angiomyolipomas were stable in 24-month follow-up. Conclusions Most patients of bilateral multifocal renal angiomyolipomas accompanied by tuberous sclerosis were symptom free, and the tumors seemed stable in size, can be treated conservatively with annual computerized tomography. Selective renal arterial embolization is the first choice of intervention, but should be reserved until symptoms develop.

关 键 词：错构瘤 结节性硬化症 肾 

分 类 号：R737.11[医药卫生—肿瘤] R744.51[医药卫生—临床医学]