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作 者:郑维红[1] 彭锋[1] 刘肇绩[1] 黄琼华[1]
机构地区:[1]厦门大学附属中山医院(福建医科大学教学医院)神经内科,福建省厦门市361004
出 处:《中国全科医学》2011年第3期311-312,共2页Chinese General Practice
基 金:福建厦门市科技局资助项目(3502Z20084019)
摘 要:目的加深对发作性运动诱发性运动障碍(paroxysmal kinesigenic dyskinesia,PKD)的认识。方法对7例PKD患者的临床资料进行分析,总结PKD的临床特征和治疗方法。结果 7例患者均为散发病例,平均发病年龄约12岁。主要表现为运动启动时突然发生异常运动,发作时意识清楚,发作间期无神经系统阳性体征,发作频繁,持续时间<1 min;抗癫痫治疗有效。结论临床中应注意PKD与癫痫的鉴别,原发性PKD抗癫痫治疗有效,一般预后良好。Objective To deepen the understanding of paroxysmal kinesigenic dyskinesia (PKD). Methods Clinical data of 7 cases with PKD were analyzed to summarize the clinical feature and treatment of PKD. Results The average onset age of 7 sporadic cases was about 12 years old. They showed abnormal movement when starting to move. The seizure happened frequently with each time less than one minute. During the seizure, there was no nervous system positive sign, and patients had clear consciousness. Treatment for anti - epilepsy proved to be effective. Conclusion PKD and epilepsy should be differentiated at clinical work, and anti - epilepsy treatment of primary PKD proves to be effective with generally good prognosis.
关 键 词:发作性运动诱发性运动障碍 临床特征 治疗 癫痫
分 类 号:R746[医药卫生—神经病学与精神病学]
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