双肾血管平滑肌脂肪瘤伴发结节性硬化症的诊治  

Diagnosis and treatment of bilateral multiple renal angiomyolipomas associated with tuberous sclerosis

作　　者：骆华[1] 卢锦山[1] 董隽[1] 

机构地区：[1]德阳市第二人民医院泌尿外科,四川618000

出　　处：《国际泌尿系统杂志》2011年第3期299-301,共3页International Journal of Urology and Nephrology

摘　　要：目的探讨双肾血管平滑肌脂肪瘤（AML）伴结节性硬化症（TSC）的临床特点，以提高该病的诊治水平。方法报告本院收治1例双肾AML伴TSC的临床诊治资料并复习文献。结果经过B超、CT及MRI检查确诊。本例女性患者双肾CT及MRI检查发现肿瘤内特异性脂肪密度组织，头颅CT检查发现典型的大脑钙化结节灶。因患者全身多发占位，手术治疗效果不佳，行保守治疗，患者定期随诊。结论B超、CT及MRI检查结合临床表现是诊断肾AML伴TSC的重要手段。其治疗方案应根据双侧肾肿瘤大小、分布。Objectives To study the clinical features of renal angiomyolipomas with tuberous sclerosis and to improve the diagnosis and treatment. Methods The diagnosis and treatment of 1 case of bilatcral multiple renal angiomyolipomas associated with tuberous scleros were reported and review the articles. Results The diagnosis of renal angiomyolipomas associated with tuberous sclerosisi was confirmed by ultrasonography and CT and MRI scanning. However. the giant renal angiomyolipomas can be diagnosed from renal CT and MRI scan which demonstrate charaeteristic fatty tissue. Brain CT revealed classical calcified cortical tuber and subependymal nodule. Regular monitoring of the patient with conservative therapy was adopted for occupying multiple body and surgical treatment results were poor. Conclusions Uhrasonography and CT and MRI are important methods to diagnose and the choice of treatment is based on tumor size, distribution pattern, symptoms and associated progression.

关 键 词：肾肿瘤 血管肌脂瘤 结节性硬化症 

分 类 号：R737.11[医药卫生—肿瘤]