Atlanto-axial langerhans cell histiocytosis in a child presented as torticollis  

作　　者：Miniar Tfifha Mehdi Gaha Nadia Mama Mohamed Taher Yacoubi Saoussen Abroug Hela Jemni 

机构地区：[1]Pediatrics Department,Sahloul University Hospital [2]Radiology Department,Sahloul University Hospital [3]Pathology Department,Farhat Hached University Hospital

出　　处：《World Journal of Clinical Cases》2017年第8期344-348,共5页世界临床病例杂志

摘　　要：Langerhans cell histiocytosis(LCH) is a rare condition mostly seen in children and adolescents. Eosinophilic granuloma(EG) is one of its three clinical entities and is considered as a benign osteolytic lesion. Many reports of patients with spine histiocytosis are well documented in the literature but it is not the case of atlantoaxial localization. We report here a new observation of atlantoaxial LCH in a 4-year-old boy revealed by persistent torticollis. He was successfully treated with systemic chemotherapy and surgery. Inter-body fusion packed by autologous iliac bone was performed with resolution of his symptoms. It is known that conservative treatment is usually sufficient and surgery should be reserved for major neurologic defects in spine EG. In atlantoaxial lesion, surgical treatment should be frequently considered.Langerhans cell histiocytosis(LCH) is a rare condition mostly seen in children and adolescents. Eosinophilic granuloma(EG) is one of its three clinical entities and is considered as a benign osteolytic lesion. Many reports of patients with spine histiocytosis are well documented in the literature but it is not the case of atlantoaxial localization. We report here a new observation of atlantoaxial LCH in a 4-year-old boy revealed by persistent torticollis. He was successfully treated with systemic chemotherapy and surgery. Inter-body fusion packed by autologous iliac bone was performed with resolution of his symptoms. It is known that conservative treatment is usually sufficient and surgery should be reserved for major neurologic defects in spine EG. In atlantoaxial lesion, surgical treatment should be frequently considered.

关 键 词：LANGERHANS cell HISTIOCYTOSIS EOSINOPHILIC GRANULOMA TORTICOLLIS Cervical spine 

分 类 号：R725.9[医药卫生—儿科]