Successful spinal anesthesia in a patient with mucopolysaccharidosis type I under femoral fracture reduction and external fixation  

作　　者：Lan Sun Jianmin Zhang Xin Zhao 

机构地区：[1]Department of Anesthesiology,Beijing Children’s Hospital,Capital Medical University,National Center for Children’s Health,Beijing,China

出　　处：《Pediatric Investigation》2019年第1期55-57,共3页儿科学研究（英文）

摘　　要：Introduction:Mucopolysaccharidosis(MPS)is an inherited lysosomal storage disorders with glycosaminoglycans accumulation in tissues.MPS patients undergoing intratracheal intubation anesthesia show high mortality,with serious anesthetic complications associated with airway thickness and narrow.The regional anesthesia is a useful alternative to general anesthesia,however performing spinal anesthesia in MPS patients are rarely documented.Case presentation:We report a case of a boy with MPS type I undergoing femoral reduction and external fixation under spinal anesthesia in combination with sevoflurane inhalational induction,getting rid of difficulties associated with intubation.Conclusion:Sevoflurane inhalational induction with spinal anesthesia without tracheal intubation is a safe choice for MPS I patient.

关 键 词：MUCOPOLYSACCHARIDOSIS CHILDREN Spinal anesthesia SEVOFLURANE Airway management 

分 类 号：TP[自动化与计算机技术]