Cerebral proliferative angiopathy in pediatric age presenting as neurological disorders:A case report  

作　　者：Fu-Ren Luo Ying Zhou Zhong Wang Qi-Yu Liu 

机构地区：[1]Department of Radiology,The Affiliated Hospital of Southwest Medical University,Luzhou 646000,Sichuan Province,China [2]Department of Radiology,Mianyang Central Hospital,Mianyang 621000,Sichuan Province,China

出　　处：《World Journal of Clinical Cases》2023年第33期8071-8077,共7页世界临床病例杂志

摘　　要：BACKGROUND Cerebral proliferative angiopathy(CPA)is a rare subtype of arteriovenous malformation.It is extremely rare in pediatric patients and has serious implications for developing children.However,reports of these disorders worldwide are limited,and no uniform reference for diagnosis and treatment options exists.We report the case of a 6-year-old with CPA having predominantly neurological dysfunction and review the literature on pediatric CPA.CASE SUMMARY We report the case of a pediatric patient with CPA analyzed using digital subtraction angiography(DSA)who presented initially with a neurological disorder as the main manifestation.This case is the basis for further discussion of the clinical presentation,pathogenesis,diagnosis,and treatment of CPA in children.After the cerebral DSA,the patient was treated conservatively with sedation,fluid replacement,and blood anticoagulation.She could not cooperate with the followup magnetic resonance imaging examination because of her young age,and her family declined further treatment because of the surgery’s high risk.She was followed up for 3 months;her symptoms did not worsen.CONCLUSION This report of rare pediatric CPA can inform and advance clinical research on congenital cerebrovascular diseases.

关 键 词：Pediatric cerebral proliferative angiopathy PATHOGENESIS Diagnosis Treatment Case report 

分 类 号：R743[医药卫生—神经病学与精神病学]