Zinner’s Syndrome: A Confusing Diagnosis in the Face of Chronic Disabling Perineoscrotal Pain in the Young Subject, about a Case  

作　　者：Ntambwe Nkashama Jean-Louis Mouhssine Errehan Kwizera Juvenal Mamoutou Mody Keita Lakmichi Mohamed Amine Dahami Zakaria Moudouni Mohamed Sarf Ismail Ntambwe Nkashama Jean-Louis;Mouhssine Errehan;Kwizera Juvenal;Mamoutou Mody Keita;Lakmichi Mohamed Amine;Dahami Zakaria;Moudouni Mohamed;Sarf Ismail(Service d’Urologie, Chu Mohamed Vi De Marrakech, Marrakech, Maroc)

机构地区：[1]Service d’Urologie, Chu Mohamed Vi De Marrakech, Marrakech, Maroc

出　　处：《Case Reports in Clinical Medicine》2021年第5期141-145,共5页临床医学病理报告（英文）

摘　　要：Zinner syndrome is a rare congenital malformation related to an abnormality in the development of the Wolffian duct, the clinical picture of which consists of a triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and obstruction of the ejaculatory duct. Chronic perineoscrotal pain may be an indication of the diagnosis of Z<span style="white-space:nowrap;">&iuml;</span>nner syndrome to some extent. We report the observation of a 23-year-old patient, married and father of one child, who presented with chronic perineo-scrotal pain revealing on morphological assessment (ultrasound, uroscanner, prostatic MRI) a cystic formation of the seminal vesicle, left renal agenesis with an empty left renal compartment. Given the patient’s refusal of any surgical procedure, treatment consisted of echo-guided puncture of the seminal vesicle cyst bringing back 30 cc of a seroviscous liquid whose analysis revealed spermatozoa, without atypical cells, compatible with a cyst. The clinical evolution was marked by a progressive remission of the scrotal pain with a delay of several months.Zinner syndrome is a rare congenital malformation related to an abnormality in the development of the Wolffian duct, the clinical picture of which consists of a triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and obstruction of the ejaculatory duct. Chronic perineoscrotal pain may be an indication of the diagnosis of Z<span style="white-space:nowrap;">&iuml;</span>nner syndrome to some extent. We report the observation of a 23-year-old patient, married and father of one child, who presented with chronic perineo-scrotal pain revealing on morphological assessment (ultrasound, uroscanner, prostatic MRI) a cystic formation of the seminal vesicle, left renal agenesis with an empty left renal compartment. Given the patient’s refusal of any surgical procedure, treatment consisted of echo-guided puncture of the seminal vesicle cyst bringing back 30 cc of a seroviscous liquid whose analysis revealed spermatozoa, without atypical cells, compatible with a cyst. The clinical evolution was marked by a progressive remission of the scrotal pain with a delay of several months.

关 键 词：AGENESIS Congenital Malformation KIDNEY Perineoscrotal Pain Seminal Vesicles Zinner’s Syndrome 

分 类 号：R73[医药卫生—肿瘤]