Mandibular Embryonal Rhabdomyosarcoma Confused with a Vascular Malformation: About a Case  

作　　者：Massilia Bouhmidi Hajar Boudarbala Ayad Ghannam Aziza Elouali Abdeladim Babakhouya Maria Rkain Noufissa Benajiba Massilia Bouhmidi;Hajar Boudarbala;Ayad Ghannam;Aziza Elouali;Abdeladim Babakhouya;Maria Rkain;Noufissa Benajiba(Mother-Child Hospital, CHU Mohamed VI, Oujda, Morroco)

机构地区：[1]Mother-Child Hospital, CHU Mohamed VI, Oujda, Morroco

出　　处：《Journal of Biosciences and Medicines》2023年第6期103-107,共5页生物科学与医学（英文）

摘　　要：Malignant mesenchymal tumors (MTM) in children represent 5% to 10% of malignant tumors in children. They constitute a heterogeneous group of tumors of various differentiations depending on their supposed tissue of origin. They mainly include tumors of muscular origin, those derived from connective, vascular, nervous, or adipose tissue. Rhabdomyosarcoma (RMS) is the most common mesenchymal tumor in children and adolescents (60% to 70% of them). And it accounts for 5.8% of all malignant solid tumors in children. Almost half of rhabdomyosarcomas occur in the head and neck. The prognosis for this type of tumor is particularly poor. A case of rhabdomyosarcoma in the mandible with extension to the abdominal wall and unilateral testis in a 6-month-old infant is reported with evolution since birth. It is a purplish lesion at the level under the right chin which was initially taken for vascular malformation, evolving very quickly towards a mandibular mass deforming the painful face with inflammatory signs, followed by the appearance of a hard swelling under the skin on the left flank taking on the same aspect of the mandibular mass. This observation illustrates the need to know how to systematically think about tumor causes in the face of atypical aspects and to carry out an anatomopathological examination.Malignant mesenchymal tumors (MTM) in children represent 5% to 10% of malignant tumors in children. They constitute a heterogeneous group of tumors of various differentiations depending on their supposed tissue of origin. They mainly include tumors of muscular origin, those derived from connective, vascular, nervous, or adipose tissue. Rhabdomyosarcoma (RMS) is the most common mesenchymal tumor in children and adolescents (60% to 70% of them). And it accounts for 5.8% of all malignant solid tumors in children. Almost half of rhabdomyosarcomas occur in the head and neck. The prognosis for this type of tumor is particularly poor. A case of rhabdomyosarcoma in the mandible with extension to the abdominal wall and unilateral testis in a 6-month-old infant is reported with evolution since birth. It is a purplish lesion at the level under the right chin which was initially taken for vascular malformation, evolving very quickly towards a mandibular mass deforming the painful face with inflammatory signs, followed by the appearance of a hard swelling under the skin on the left flank taking on the same aspect of the mandibular mass. This observation illustrates the need to know how to systematically think about tumor causes in the face of atypical aspects and to carry out an anatomopathological examination.

关 键 词：RHABDOMYOSARCOMA MANDIBLE Mesenchymal Tissue Vascular Malformation Abdominal Wall TESTIS 

分 类 号：R73[医药卫生—肿瘤]