妊娠期阵发性睡眠性血红蛋白尿症1例报告并文献复习  

Paroxysmal nocturnal hemoglobinuria during pregnancy:a case report and literature review

作　　者：王蔚[1] 王小钦[1] Wang Wei;Wang Xiaoqin(Huashan Hospital Affiliated to Fudan University,Shanghai 200040,China)

机构地区：[1]复旦大学附属华山医院,上海200040

出　　处：《中华血液学杂志》2024年第9期861-863,共3页Chinese Journal of Hematology

摘　　要：阵发性睡眠性血红蛋白尿症(PNH)为罕见病,妊娠期妇女的规范化治疗和随访管理对于孕产妇和新生儿的安危都非常重要。本文报告1例依库珠单抗治疗后顺利产子的妊娠期PNH患者,并对妊娠期PNH患者的治疗方案和随访管理进行总结,旨在提高孕产妇PNH的治疗水平。Paroxysmal nocturnal hemoglobinuria (PNH) is a rare disease, and a standardized treatment and follow-up management strategy for pregnant women with this disease are crucial for ensuring the safety of both the mothers and their newborns. This study includes a case of pregnant women with PNH. In accordance with the guidelines, the patient was successfully delivered after treatment with eculizumab. Furthermore, this study also implemented a treatment plan and follow-up management plan for PNH patients during pregnancy to elevate the standard of care for pregnant women with PNH.

关 键 词：阵发性睡眠性血红蛋白尿症 妊娠期妇女 随访管理 罕见病 规范化治疗 PNH 孕产妇 依库珠单抗 

分 类 号：R714.25[医药卫生—妇产科学]