Meningeal Hemangiopericytoma: A Rare Intracranial Tumor—About a Case  

作　　者：Aboubacar Sidiki Keita Mamadou Diallo Adama Dembele Mamadou Cisse Aboubacar Sidiki Keita;Mamadou Diallo;Adama Dembele;Mamadou Cisse(Medical Imaging Department, Hôpital Nord Franche Comté, Trevenans, France;Faculty of Health Sciences and Techniques of Gamal Abdel Nasser University, Conakry, Guinea;Medical Imaging Department, Centre Hospitalier Intercommunal Elbeuf Louviers, Rouen, France;Medical Imaging Department, Centre Hospitalier de Blois, Tours, France)

机构地区：[1]Medical Imaging Department, Hô pital Nord Franche Comté, Trevenans, France [2]Faculty of Health Sciences and Techniques of Gamal Abdel Nasser University, Conakry, Guinea [3]Medical Imaging Department, Centre Hospitalier Intercommunal Elbeuf Louviers, Rouen, France [4]Medical Imaging Department, Centre Hospitalier de Blois, Tours, France

出　　处：《Case Reports in Clinical Medicine》2022年第9期386-392,共7页临床医学病理报告（英文）

摘　　要：Introduction: Hemangiopericytoma is a very rare vascular tumor, difficult to diagnose, often confused with a meningioma. Imaging is not very specific and the diagnostic certainty remains histological. Observation: We report a case of meningeal hemangiopericytoma in a 48-year-old patient with a history of active smoking and whose sister died of glioblastoma. He was brought to the emergency room for a fall, confusion, and tonic-clonic seizures. The diagnosis was suspected on imaging (CT and MRI, in front of a syndrome of right temporal intraventricular mass measured at 37 mm in diameter, centered on the choroid plexus, with perilesional vasogenic edema and posterior white commissure. There was homogeneous enhancement of the lesion after gadolinium injection. The diagnosis was confirmed by immunohistochemical study, which showed diffuse expression of STAT6 and partial labeling for CD34, without significant expression of SSTR2. Expression of neurofilament protein was also found in the brain parenchyma. Conclusion: Hemangiopericytoma is a rare tumor, characterized by its malignant potential, its high rate of recurrence and distant metastasis. The management is based on a total microsurgical resection followed by radiotherapy.Introduction: Hemangiopericytoma is a very rare vascular tumor, difficult to diagnose, often confused with a meningioma. Imaging is not very specific and the diagnostic certainty remains histological. Observation: We report a case of meningeal hemangiopericytoma in a 48-year-old patient with a history of active smoking and whose sister died of glioblastoma. He was brought to the emergency room for a fall, confusion, and tonic-clonic seizures. The diagnosis was suspected on imaging (CT and MRI, in front of a syndrome of right temporal intraventricular mass measured at 37 mm in diameter, centered on the choroid plexus, with perilesional vasogenic edema and posterior white commissure. There was homogeneous enhancement of the lesion after gadolinium injection. The diagnosis was confirmed by immunohistochemical study, which showed diffuse expression of STAT6 and partial labeling for CD34, without significant expression of SSTR2. Expression of neurofilament protein was also found in the brain parenchyma. Conclusion: Hemangiopericytoma is a rare tumor, characterized by its malignant potential, its high rate of recurrence and distant metastasis. The management is based on a total microsurgical resection followed by radiotherapy.

关 键 词：Intracranial Meningeal Hemangiopericytoma Surgery METASTASIS RADIOTHERAPY 

分 类 号：R73[医药卫生—肿瘤]