FABRY

作品数:181被引量:386H指数:10
导出分析报告
相关领域:电子电信医药卫生更多>>
相关作者:孙东松陈楠陈佳韵王朝晖王伟铭更多>>
相关机构:中国科学院上海交通大学医学院附属瑞金医院北京大学第一医院中国科学技术大学更多>>
相关期刊:更多>>
相关基金:国家自然科学基金国家高技术研究发展计划国家重点基础研究发展计划重庆市自然科学基金更多>>
-

检索结果分析

结果分析中...
条 记 录,以下是1-10
视图:
排序:
Fabry肾病诊治进展
《临床内科杂志》2025年第2期101-104,共4页杨林晖 李月红 
北京市医院管理中心临床医学发展专项“扬帆计划”资助项目(YGLX202332);住院医师规范化培训质量提高项目(Z10600202451)。
Fabry病是一种罕见的遗传性代谢性疾病,主要是由于α-半乳糖苷酶A缺乏引起的脂质沉积,导致多器官功能障碍,尤其是肾脏,常见的临床表现为肾功能渐进性损害。疾病的诊断复杂性和临床表现的多样性,使其早期诊断和治疗均面临挑战。本文主要...
关键词:FABRY病 Α-半乳糖苷酶A 肾功能损害 
基于双波长强度调制的法布里-珀罗滤光器中心波长定标
《光学学报》2024年第24期177-184,共8页朱瑾 马琳 金振宇 穆恒宇 
国家自然科学基金(12073074,11833010);国家重点研发计划(202103AD50013);云南省科技计划项目(202105AB160001);云南省科技人才与平台计划(202305AH340002);云南省兴滇英才人才培养计划(202305AS350029)。
法布里-珀罗(F-P)滤光器是太阳二维成像光谱观测系统的重要组成部分,为了实现高精度太阳二维成像光谱观测,要求F-P滤光器必须具有准确的中心波长。由于滤光器只能提供控制器数值,无法直接获取波长信息,提出一种基于双波长强度调制的定...
关键词:Fabry‒Perot滤光器 定标 腔长 中心波长 双波长强度调制 
Chaotic oscillator in frequency domain with fiber Fabry⁃Perot interferometer
《黑龙江大学工程学报(中英俄文)》2024年第4期40-46,共7页WANG Huiying LI Chuandi LV Guohui 
黑龙江省自然科学基金项目(A200604);国家自然科学基金项目(60077007)
Chaos is a type of motion unique to nonlinear dynamical systems,characterized by extreme sensitivity to initial conditions and the randomness,which makes it potentially useful for secure communication.Chaos research r...
关键词:tunable fiber laser fiber Fabry⁃Perot interferometer delayed feedback chaotic oscillator in frequency domain 
Two-photon 3D printed fiber-optic Fabry–Perot probe for triaxial contact force detection of guidewire tips
《Photonics Research》2024年第11期2474-2487,共14页RUIXUE YIN YUHANG YANG LINSONG HOU HEMING WEI HONGBO ZHANG WENJUN ZHANG 
Foundation of National Center for Translational Medicine(Shanghai)SHU Branch(SUITM-2023010);National Natural Science Foundation of China(62005153)。
The demand for real-time feedback and miniaturization of sensing elements is a crucial issue in the treating vascular diseases with minimally invasive interventions.Here,Fabry–Perot microcavities fabricated via direc...
关键词:sectional utilized compatibility 
Bridging the Fabry–Perot cavity and asymmetric Berreman mode for long-wave infrared nonreciprocal thermal emitters
《Science China(Technological Sciences)》2024年第10期3285-3293,共9页CHEN ZiHe YU ShiLv HU Run 
supported by the National Natural Science Foundation of China(Grant Nos.52211540005 and 52076087);the Natural Science Foundation of Hubei Province(Grant No.2023AFA072);the Open Project Program of Wuhan National Laboratory for Optoelectronics(Grant No.2021WNLOKF004);Wuhan Knowledge Innovation Shuguang Program,and the Fundamental Research Funds for the Central Universities(Grant No.YCJJ20242102).
The long-wave infrared band(8–14μm)is essential for several applications,such as infrared detection,radiative cooling,and near-field heat transfer.However,according to Kirchhoff’s law,the intrinsic balance between ...
关键词:long-wave infrared band nonreciprocal thermal radiation sandwich structure Fabry–Perot cavity asymmetric berreman mode 
Filter-free high-performance single-photon emission from a quantum dot in a Fabry–Perot microcavity
《Photonics Research》2024年第10期2130-2138,共9页JIAWEI YANG ZHIXUAN RAO CHANGKUN SONG MUJIE RAO ZIYANG ZHENG LUYU LIU XUEBIN PENG YING YU SIYUAN YU 
Key R&D Program of Guangdong Province(2020B0303020001);National Natural Science Foundation of China(12074442);Innovation Program for Quantum Science and Technology(2021ZD0301400);Science and Technology Program of Guangzhou(202103030001)。
Combining resonant excitation with Purcell-enhanced single quantum dots(QDs)stands out as a prominent strategy for realizing high-performance solid-state single-photon sources.However,optimizing photon extraction effi...
关键词:RESONANT quantum EXCITATION 
Multiple wavelength frequency stabilization with a single transfer cavity for mercury optical lattice clock
《Chinese Optics Letters》2024年第10期100-105,共6页Li Ma Qixin Liu Haiyang Song Jianfang Sun Zhen Xu 
supported by the National Natural Science Foundation of China(Nos.11874371,91436105,and 12104474);the Shanghai Science and Technology Program,China(No.22ZR1471000);the Strategic Pilot Science and Technology Project of the Chinese Academy of Sciences,China(No.XDB21030200)。
A simple and robust multiple wavelength frequency stabilization system is demonstrated using a single transfer cavity and a1062-nm ultra-stable laser for all the lasers used in a mercury optical lattice clock.Offset s...
关键词:laser frequency stabilization Fabry–Perot cavity optical lattice clock Pound–Drever–Hall locking 
Mode coupling with Fabry-Perot modes in photonic crystal slabs
《Chinese Physics B》2024年第8期90-94,共5页秦恳 胡鹏 刘杰 向红 韩德专 
Project supported by the National Natural Science Foundation of China (Grant Nos.12074049 and 12347101)。
Fabry–Perot(FP)modes are a class of fundamental resonances in photonic crystal(PhC)slabs.Owing to their low quality factors,FP modes are frequently considered as background fields with their resonance nature being ne...
关键词:Fabry–Perot mode photonic crystal slab mode coupling exceptional point 
Miniaturized and highly sensitive fiber-optic Fabry–Perot sensor for mHz infrasound detection被引量:1
《Photonics Research》2024年第5期969-978,共10页PEIJIE WANG YUFENG PAN JIANGSHAN ZHANG JIE ZHAI DEMING LIU PING LU 
Science Fund for Creative Research Groups of the Nature Science Foundation of Hubei(2021CFA033);National Natural Science Foundation of China(62275096);Interdisciplinary Research Program(HUST:2023JCYJ046)。
Infrasound detection is important in natural disasters monitoring,military defense,underwater acoustic detection,and other domains.Fiber-optic Fabry–Perot(FP)acoustic sensors have the advantages of small structure si...
关键词:SOUND fiber CAVITY 
法布里病(Fabry 病)致反复晕厥误诊癫痫1例病例报道
《云南医药》2024年第2期109-110,共2页杨娅梅 
法布里病(Fabry病)是罕见的遗传性溶酶体贮积症,可累及心肌及心脏传导系统,现将本科室误诊1例患者,临床资料报道如下。
关键词:FABRY病 累及心脏传导系统及心肌肥厚 
检索报告 对象比较 聚类工具 使用帮助 返回顶部