云南高校图书馆联盟文献共享服务平台- HEMOPHAGOCYTIC

HEMOPHAGOCYTIC: 作品数：18被引量：20H指数：3; 导出分析报告; 相关领域：医药卫生更多>>; 相关机构：广州市妇女儿童医疗中心上海交通大学更多>>; 相关期刊：《Chinese Medical Journal》《Open Journal of Genetics》《World Journal of Hematology》《World Journal of Gastroenterology》更多>>; 相关基金：国家自然科学基金北京市自然科学基金更多>>

Chediak-Higashi Syndrome Diagnosed from Mutation Carriers: 《Open Journal of Genetics》2024年第4期87-91,共5页Kouamé Cyprien Kouakou Augustine Djivohessoun Isabelle Djoman Andre Marius Gro-Bi Charlène Soro Komenan Amoro Mansou Stella Nyango Amorissani Folquet; We report a case of a 9-month-old girl diagnosed as heterozygous to the Chediak-Higashi syndrome (CHS) after the death of her four brothers, who had similar symptoms of severe anemia, recurrent infections, and multipl...; 关键词：Chediak-Higashi Syndrome INBREEDING Genetic Counseling HEMOPHAGOCYTIC LYMPHOPROLIFERATION

Managing adult-onset Still's disease in pregnancy:A case report: 《World Journal of Clinical Cases》2024年第16期2837-2841,共5页Ji-Hyoun Kang; BACKGROUND Adult-onset Still’s disease(AOSD)is a rare systemic inflammatory disorder characterized by fever,arthritis,skin rash,and systemic symptoms.The etiology of AOSD is unknown;however,it is thought to be relate...; 关键词：NEONATE Hemophagocytic lympho-histiocytosis Adult-onset Still’s disease PREGNANCY Case report

Hemophagocytic lymphohistiocytosis complicated by polyserositis:A case report: 《World Journal of Clinical Cases》2019年第19期3069-3073,共5页Ping Zhu Qing Ye Ting-Hong Li Tao Han Feng-Mei Wang; BACKGROUND Hemophagocytic lymphohistiocytosis(HLH)is a rare group of disorders of immune dysregulation characterized by clinical symptoms of severe inflammation.There are basically two types of clinical scenarios:Fami...; 关键词：HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Polyserositis LIVER INJURY FEVER Case report

Detection of Th17/Treg balance in peripheral blood of children with hemophilia syndrome and its correlation with severity: 《Journal of Hainan Medical University》2019年第5期58-60,共3页Wei-Juan Lei Jie Pan; Objective:To investigate the relationship between Th17/Treg balance in peripheral blood and severity of hemophagocytic syndrome in children.Methods:A total of 60 children with HLH diagnosed in our hospital were taken ...; 关键词：HEMOPHAGOCYTIC SYNDROME TH17/TREG SF Inflammatory MEDIATORS

Neurological Abnormality Could be the First and Only Symptom of Familial Hemophagocytic Lymphohistiocytosis: Report of Two Families被引量：1: 《Chinese Medical Journal》2018年第24期3004-3006,共3页Yun-Ze Zhao Hua Cheng Chang-Hong Ding Hong-Hao Ma Tong-Li Han Jiu-Wei Li Dong Wang Zhi-Gang Li Tian-You Wang Rui Zhang; the grants from the National Science and Technology Key Projects (No.2017ZX09304029004);Beijing Municipal Science and Technology Commission (No.Z 171100001017050);National Natural Science Foundation of China (No.81700186,81800189);Scientific Research Common Program of Beijing Municipal Commission of Education (No.KM201710025019);Talent Training Proj ect-Fostering Fund of National Natural Science Foundation of Beijing Children's Hospital,Capital Medical University (No.GPY201713);The Special Fund of The Pediatric Medical Coordinated Development Center of Beijing Municipal Administration (XTZD20180202).; To the Editor:Hemophagocytic lymphohistiocytosis (HLH)is a life-threatening disease which impacts many parts of the body including the digestive,circulatory,and respiratory systems.The central nervous system (CNS)can ...; 关键词：NEUROLOGICAL ABNORMALITY SYMPTOM of FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS

Haploidentical hematopoietic stem cell transplantation using reduced-intensity conditioning for pediatric patients with familial hemophagocytic lymphohistiocytosis被引量：1: 《Pediatric Investigation》2018年第4期216-221,共6页Chenguang Jia Bin Wang Guanghua Zhu Rui Zhang Kai Wang Yan Yan Maoquan Qin; Importance: Allogeneic hematopoietic stem cell transplantation (HSCT) is considered to be the only curative treatment for familial hemophagocytic lymphohistiocytosis (FHLH). Treatment of pediatric FHLH with reduced-in...; 关键词：HAPLOIDENTICAL HEMATOPOIETIC stem cell transplantation HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS PEDIATRIC Reduced intensity CONDITIONING

Nodular Panniculitis with Hemophagocytic Lymphohistiocytosis被引量：3: 《Chinese Medical Journal》2018年第23期2860-2861,共2页Huan Liu Yi-Dan Chen Yang Wu Geng Yin Qi-Bing Xie; grants from National Natural Science Foundation of China (No.30901339and No.81172869); the Application Foundation Project in Sichuan Province (No.2016JY0021and No.2017JY0025).; To the Editor:A 27-year-old Chinese man presented to the hospital complaining of red nodules on the chest and back that gradually enlarged with spiking fever up to 39℃.He had nodular panniculitis when he was 21 years...; 关键词：NODULAR PANNICULITIS HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS

Finding the perfect recipe for success: 《Pediatric Investigation》2018年第4期222-222,共1页Theodore B.Moore; Familial hemophagocytic lymphohistiocytosis (FHLH) is a rare genetic disease for which optimal therapy includes consolidation with a hematopoietic stem cell transplant (HSCT). The HLH-1994 study demonstrated a 3-year ...; 关键词：PERFECT RECIPE SUCCESS FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS

Acute liver failure secondary to severe systemic disease from fatal hemophagocytic lymphohistiocytosis:Case report and systematic literature review被引量：6: 《World Journal of Hepatology》2018年第9期629-636,共8页Mitchell S Cappell Ismail Hader Mitual Amin; AIM To systematically review liver disease associated with hemophagocytic lymphohistiocytosis(HLH),propose reasonable contraindications for liver transplantation for liver failure in HLH,and report an illustrative cas...; 关键词：HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Acute LIVER failure LIVER injury LIVER transplantation Acquired immune HYPERACTIVATION PANCYTOPENIA

Successful rescue of acute liver failure and hemophagocytic lymphohistiocytosis following varicella infection: A case report and review of literature被引量：6: 《World Journal of Clinical Cases》2018年第13期659-665,共7页Li-Na Zhang Wei Guo Ji-Hong Zhu Yang Guo; Supported by Capital Characteristic Clinic Project,No.Z161100000516045; Herein we report a case of acute liver failure(ALF) and hemophagocytic lymphohistiocytosis(HLH) induced by varicella infection, successfully rescued by a combination therapy of acyclovir, supportive care, and immunosu...; 关键词：Acute liver failure Immune DYSREGULATION HYPERFERRITINEMIA HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS VARICELLA INFECTION Skin rash

HEMOPHAGOCYTIC